Iranian Society of Gynecology Oncology

Document Type : Case Report Article

Authors

1 School of Medicine, Imam Hossein hospital, Iran University of Medical Sciences, Tehran, Iran

2 Department of Obstetrics and Gynecology, Shahid Beheshti University of Medical Sciences, Tehran, Iran

3 Department of Biology, Science and Research University of Tehran, Tehran, Iran

4 Department of Obstetrics and Gynecology, Imam Hossein Medical Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran

5 Department of Radiology, Imam Hossein Medical Center, Shahid Beheshti University of Medical Sciences, Tehran, Iran

6 Department of Surgery, Imam Hossein Hospital, Shahid Beheshti University of Medical Sciences, Tehran, Iran

7 Department of Obstetrics and Gynecology, Tehran University of Medical Sciences, Tehran, Iran

Abstract

Background & Objective: Low-grade appendiceal mucinous neoplasm (LAMN) is a very rare condition, diagnosed in 0.2-0.7% of appendectomies. The pathophysiology of the neoplasm involves accumulation of large volume of mucin in the appendiceal lumen, resulting in its obstructive dilation. Most epithelial tumors affecting the appendix are of the mucinous type and are manifested by mucin accumulation within an inflamed appendix with fibrotic and hyalinized wall.
Case Presentation: A 29-year-old female presented with a history of chronic and intermittent episodes of abdominal pain and a palpable mass in the right lower abdominal quadrant. Sonography showed a 58 mm mass anterior to the uterus and adjacent to the ovary, probably a uterine myoma. Laparotomy revealed normal uterus, and ovaries with a translucent mass originating from the appendix and fixed to the cecum. Pathologic examination of the mass was reported as low grade appendiceal mucinous neoplasm.
Conclusion: This is a rare case of appendiceal mucocele in a young female, mimicking a pelvic mass, which was misinterpreted by sonography as a gynecologic solid mass near the uterus. Preoperative diagnosis of appendiceal mucocele is important due to the risk of concurrent GI and ovarian malignancy associated with the condition.

Highlights

 This is a rare case of appendiceal mucocele in a young female, mimicking a pelvic mass, which was misinterpreted by sonography as a gynecologic solid mass near the uterus. Preoperative diagnosis of appendiceal mucocele is important due to the risk of concurrent GI and ovarian malignancy associated with the condition.

Keywords

Main Subjects

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